SGSH Rabbit mAb

产品详情

产品名称

SGSH Rabbit mAb

产品货号

YM-A25338

规格

50μL;100μL

种属反应

Human

实验应用

WB,IHC,IF,ICC

分子量

55kD

宿主

Rabbit

同种型

IgG,Kappa

修饰

推荐稀释比

WB 1:1000-5000;IHC 1:100-300;ICC/IF 1:100-300

组成

PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA

纯化工艺

Protein A

储存

-15°C to -25°C/1 year(Do not lower than -25°C)

浓度

克降性

克隆号

PT0814R

免疫原

特异性

Endogenous

基因名称

SGSH;HSS

蛋白名称

N-sulphoglucosamine sulphohydrolase;Sulfoglucosamine sulfamidase;Sulphamidase;

别名

SGSH;HSS;N-sulphoglucosamine sulphohydrolase ;Sulfoglucosamine sulfamidase;Sulphamidase;

基因ID-1

6448

SwissProt

P51688

背景

This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]

细胞定位

Lysosome.